Noj qab haus huvCov kab mob thiab mob

Myopathy kab mob - yog dab tsi?

Muaj coob tus tau hnov txog tus kab mob no li myopathy. Yuav ua li cas yog nws, paub tsis txhua leej txhua tus. Lub sij hawm "myopathy" combines ib tug xov tooj ntawm niam txiv cov kab mob nyob rau hauv uas ntxhov contractile muaj peev xwm ntawm cov nqaij fibers thiab npaj nqaij tsis muaj zog. Raws li ib tug tshwm sim, ib tug txo nyob rau hauv lub ntim ntawm active taw, laus txo, Atrophy, thiab nyob rau hauv tej rooj plaub psevdogipertrofiya leeg. Tsis tas li ntawd nyob rau hauv myopathy to taub tag nrho skeletal leeg pathology. Tus kab mob feem ntau yog raws roj ntsha xwm, tab sis kuj los muaj kev raws li ib tug tshwm sim ntawm kev raug mob los yog kab mob. Ntau susceptible mus rau myopathy caug.

Myopathy - dab tsi yog nws thiab dab tsi yog qhov txawv ntau yam ntawm tus kab mob?

Ib tug ntau yam ntawm cov ntaub ntawv kab mob yog enormous. myopathy nram qab no yog cov feem ntau:

  • Duchenne;

  • Landuzi-Dejerine;

  • Becker;

  • Erb thiab Erb-Rot;

  • Amyotrophy Werding-Hoffmann;

  • Amyotrophy Kugelberg-Welander li al.

Qhov loj tshaj plaws thiab feem ntau zoo-paub hauv daim ntawv ntawm tus kab mob no yog Duchenne lub myopathy. Nws yog yus muaj los ntawm ib tug niam txiv defect ntawm lub dystrophin - ib tug protein uas koom tes rau kev ncaj ncees ntawm nqaij fibers. Nyob rau hauv daim ntawv no ntawm tus kab mob no muaj ib tug ua tiav tsis muaj nws.

Myopathy: cov tsos mob

Lub ntsiab seb mob dab tsi ntawm tus kab mob loj heev nqaij tsis muaj zog. Tej zaum nws yuav ua tau cov kev hloov ntawm adipose cov nqaij mos nqaij fibers, uas ua rau yus mus rau lawv hypertrophy. Lawv ua nyeem tas thiab ib qho nyuaj rau cov kov thiab ywj. Rau cov neeg mob nrog myopathy moj yam yam ntxwv waddle. Feem ntau, tsis muaj zog intensified nyob rau hauv 8-10 hom xyoos. Cov me nyuam yuav nyuaj mus kev, thiab qhov no muaj peev xwm poob zoo rau nws rau 12 xyoo. Thaum lub sij hawm no lub sij hawm pib mus rau daim ntawv yog qhov khoov pob, ob leeg contractures, uas yog kho kom zoo los ntawm zuj zus lawm kev ua si. Ib txhia neeg mob ncua kev puas hlwb txoj kev loj hlob muaj peev xwm muaj cai nyob rau hauv lub tom qab ua sawv ntawm lub plawv tsis ua hauj lwm. Cov neeg nyob nrog no mob ib tug nruab nrab ntawm txog 20 xyoo. Lub ntsiab ua rau ntawm kev tuag yog mob thiab ua pa tsis ua hauj lwm.

Myopathy: cov kev kho mob ntawm tus kab mob

Cov kev kho ntawm tus kab mob yog feem ntau aimed ntawm kev tsim kom muaj microcirculation thiab cov metabolism hauv nyob rau hauv cov nqaij thiab tshee systems. Rau lub hom phiaj no, siv cov anabolic agents, cov vitamins, tshuaj poov tshuaj, biogenic stimulants, tshuaj trophotropic txiav txim, anticholinesterase agents, vasoactive tshuaj.

Tsis tas li ntawd, Yog hais tias myopathy yog heev pab tau kho zaws ntawm lub tag nrho lub cev. Tsaug rau txoj kev ua no, ntshav yog tsa, xa cov ntshav stasis, nce ntshav txaus rau cov nqaij ntshiv. Nyob rau hauv tas li ntawd, cov zoo ntxim yog ib tug ua tau kev qoj ib ce, muab tshuaj ntxuav, kub da dej nrog cov hiav txwv ntsev.

Yog li, peb soj ntsuam lub tswvyim ntawm "myopathy", yog dab tsi thiab dab tsi yog qhov hauv paus ntsiab lus ntawm kev kho mob ntawm tus kab mob. Txawm li cas los, txawm muaj xws li ib tug mob yuav tsum tau ua raws li tej yam yus noj. Nws yuav cov cais tawm ntawm dej cawv haus, tsis pub tshaj rog, ntsim, qab ntsev cov khoom noj, thiab nqaij. Pom zoo kom tsawg ntawm cov mis nyuj nyob rau hauv unlimited qhov ntau, kav xam lav, cereals dej los ntawm germinated grain cereals, apples, daim siab, sunflower roj thiab cov hiav txwv buckthorn.

Tam sim no, Yog hais tias koj tuaj nyob lub sij hawm "myopathy", yog dab tsi, tom qab nyeem ntawv tsab xov xwm koj twb paub lawm.

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