Noj qab haus huv, Cov kab mob thiab mob
Myasthenia Heavy kev: cov tsos mob, ua rau, kev kho mob
Lo lus "Heavy kev" yog lus txhais li "nqaij tsis muaj zog". Tsis tas li ntawd lub npe tus kab mob muaj ntau ntau lwm yam: bulbar tuag tes tuag taw, ophthalmoplegia asthenic, Goldflam kab mob, pathological npag fatigue syndrome. Nws yog ib tug kab mob autoimmune. Qhov no txhais tau tias nyob rau hauv tib neeg muaj tshuaj uas ua kom puas teeb meem hlwb thiab tsis muaj kab mob, thiab tua ib txwm noj qab nyob zoo lub hlwb.
Myasthenia Heavy kev, uas yog zoo ib yam li cov tsos mob ntawm tus milestones ntawm tus neeg mob, ntau zaus muaj nyob rau hauv cov tub ntxhais cov poj niam nyob rau hauv lub hnub nyoog ntawm plaub caug xyoo. Txhua 10 cov neeg tawm ntawm ib puas txhiab hnub no yog mob myasthenia Heavy kev. Cov tsos mob ntawm tus kab mob:
• ob lub zeem muag nyob rau hauv rau yav tsaus ntuj, qhov muag nkees, tej ntawm lub hnub nyoog;
• yav tsaus ntuj txhaws qa, ligaments nkees tom qab heev lub suab loading;
• heev qaug zog ;
• Kev ua txhaum zoo lub cev muaj zog cov kev txawj;
• ib tug txo nyob rau hauv rhiab heev;
• zog mob, tshwj xeeb tshaj yog thaum lub sij hawm repetitive taw;
• nqos mob, khoom noj khoom haus los ntawm uas nkag mus rau lub qhov ntswg, qhov ntswg suab;
• chua nyob rau hauv ua tsis taus pa.
Muaj ntau mob uas sau hais tias nyob rau hauv lub tshav kub qaug zog tsub kom sharply, thiab rov qab tshwm sim sai li qaug zog.
Cov insidious myasthenia Heavy kev? Nws cov tsos mob yuav mus unnoticed rau ntau xyoo. Los ntawm qhov xwm ntawm tus kab mob no yuav ua tau nyob ruaj ruaj los yog, nyob rau hauv Feem ntau, hnyav. Nyob Ruaj Ruaj daim ntawv pom tsuas yog tias cov kev kho mob yog tsis zoo.
Progressive muaj peev xwm tsim tsis pub dhau rau lub hlis (ceev), rau lub lim tiam (ntxhib), ob lub lis piam (phem). Myasthenia Heavy kev, uas nws cov tsos mob pib acutely, muaj xws li tag nrho cov nta teev saum toj no. Thaum untimely kev kho mob ntawm phem myalgia, cov tsos mob ntawm uas yog loj hlob heev ceev ceev, yuav ua tau kom immobility.
Tus duab ntawm lub chav kawm ntawm myasthenia Heavy kev faib rau hauv lub zos (feem ntau lub qhov muag) thiab generalized daim ntawv. Myasthenia Heavy kev, generalized daim ntawv uas muaj feem xyuam rau ntau yam kabmob pab pawg neeg, thiaj paub hais tias neurological tsev kho mob. Rau mob nws yog tsim nyog los tuav ib lub computer thiab magnetic resonance tomography, pnevmomediastinografiyu, prozerinovye qauv. Thov kuj yog ib tug me ntawm npag cov ntaub so ntswg, general Somatic kev tshawb fawb, kev tshuaj ntsuam genetic ntsuam, electroneurogram.
Yog hais tias qhov mob ntawm myasthenia Heavy kev, kev kho mob yog txiav txim los ntawm peb cov loj tenets:
• Cov qib.
• Ua ke nrog ntawm ntau hom (compensating, uas tsis yog-kev, pathogenetic) txoj kev kho.
• Raug tshem tawm ntawm lub mob theem.
Thaum lub sij hawm cov nyiaj theem, cov kev kho mob feem ntau yog muab anticholinesterase tshuaj veroshpiron, neostigmine methylsulfate, poov tshuaj tshuaj dawb. Nyob rau hauv lub thib ob theem, nyob rau hauv loj heev zaum nws yuav raug muab qhia thymectomy - tshem tawm ntawm lub thymus. Nyob rau hauv 75% ntawm cov neeg, lub lag luam no ua kom tiav rov qab, nyob rau hauv lwm tus neeg - mus rau ib tug tseem ceeb kev txhim kho. Lub lag luam muaj peev xwm yuav mob los ntawm cov pa tus thiab me ntsis puas txoj kev.
Tom qab muab hlais tawm lawm (tej zaum xwb) muab glucocorticoid tshuaj. Tej kev kho mob yog dua li nqa tawm nyob rau hauv ib tug lub tsev kho mob, nyob rau hauv lub saib xyuas ntawm cov kws tshwj xeeb. Qhov thib peb theem ntawm cov kev kho mob ntawm myasthenia Heavy kev - lub sij hawm immunosuppressants.
Tsoos txoj kev los kho tus kab mob no yog tsis tau, tab sis lawv muaj peev xwm nrog lub ntsiab kev kho mob yog tias cov kws kho mob tsis txhob mloog. Piv txwv li, lub khob yuav tsum steamed oat pint ntawm dej, rhaub peb quarters ntawm ib teev, ib teev thiab ntws qhov tau nqa los zib ntab, muab nws mus rau cov kua ib nrab khob plaub zaug ib hnub twg. Lwm daim ntawv qhia yog yooj yim dua los npaj. Lub peb dhau los ntawm lub rab hau ntawm qej tov nrog ob peb tsevneeg los plaub tug txiv qaub, ntxiv ib kilo ntawm zib ntab thiab ib khob ntawm linseed roj. Cov sib tov yog coj peb lub sij hawm ib hnub twg.
Niaj kev kho mob rau myasthenia Heavy kev, koj yuav tsum nco ntsoov hais tias nws yuav pab tau yog hais tias ib tug noj qab nyob zoo txoj kev ua neej.
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